Özet:

Aplasia cutis congenita type VI (Barts syndrome), is a rare genetic disorder characterized by congenital localized absence of skin, formation of blisters (epidermolysis bullosa), and nail abnormalities. In this report, we present a rare case of aplasia cutis congenita type VI (Barts syndrome) in a newborn male baby with the absence of a skin layer over the anterior right leg, slightly below the patella (kneecap) and around the ankle joint. On the second day, the affected areas developed blisters characterizing epidermolysis bullosa. Laboratory investigations were all normal. The patients wound was managed conservatively with dressing and topical antibiotic ointments.

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