Abstract:

Interstitial lung diseases (ILDs) are a group of diffuse parenchymal lung disorders associated with considerable morbidity and mortality. These include a large number of conditions, with a wide range of underlying causes, clinical manifestations, imaging, and distinct pathological features with variable outcomes. Pulmonary fibrosis is a pathologic process that arises from multiple underlying causes. Monitoring disease progression has become a priority in guiding treatment decisions. This article aims to review pulmonary fibrosis in various interstitial lung disease entities along with underlying pathophysiological features, clinical features, diagnostic workup and current possible treatment modalities of these fibrotic lung diseases.

Keywords: