Abstract:

Acute infantile hemorrhagic edema (AIHE) is a leukocytoclastic vasculitis that is confined to the skin without visceral involvement. Edema and purpuric lesions characterize the disease. It is considered as an uncommon form of cutaneous vasculitis occurring in children younger than 2 years of age. By many authors, it is considered to be a variant of Henoch Schönlein Purpura because of similarities in causality and histopathology. In spite of its clinical violent onset, the course is often benign and spontaneous recovery is observed within several weeks. Although the etiology is unknown, AIHE often follows infections, drug treatment or vaccination. Here, a tenmonth-old girl presenting with purpuric plaques on the right buccal area and edema on the face and eye and clinically diagnosed as AIHE is presented.

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