Özet:

Autosomal dominant polycystic kidney disease (ADPKD) is an inherited systemic disorder characterized by renal cyst enlargement which results in abnormal kidney structure and renal insufficiency. The anaesthesia management of patients with ADPKD is often complex and carries considerable risks of perioperative complications. Safe and successful anaesthesia management requires an increased understanding of ADPKD pathophysiology. We report successful perioperative management of a bilateral open surgical radical nephrectomy on a male patient with giant symptomatic ADPKD. The patient had chronic renal failure and extremely large kidneys. We believe that the description and observations seen in this case will aid in the recognition and anaesthetic management of this syndrome. 

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