Özet:

Aim: Desmoid tumors originating from musculoaponeurotic tissues progress locally and aggressively and these tumors do not metastasize to distant sites. The incidence shows increase in polyposis coli syndromes. In this article, we aimed to evaluate the results of the patients treated for desmoid tumors. Method: Fifteen patients, who were diagnosed with desmoid tumors between the dates of 2000 and 2013, were evaluated in terms of demographical and clinical data, surgical interventions, complications and long-term follow-up results. Results: The median age of patients was 35 (in between 20-51 years) years and 9 (60%) of them were women. Among 13 patients with polyposis syndrome, 6 (40%) underwent restorative proctocolectomy and 5 (33%) underwent total colectomy and ileorectal anastomosis. As 2 patients were accepted as inoperable, colon-oriented surgical intervention was not performed. Following the diagnosis of polyposis coli, the mean period of time between the surgery and development of desmoid tumor was found as 24.5 months (in between 4-48 months). Intra-abdominal region was found to be the most common tumor location (n=11 patients, 74%). As eight patients (54%) were inconvenient to the surgical excision, they were accepted as inoperable when they were diagnosed with desmoid tumor. Seven patients could undergo surgical resection, but all of them had recurrence in their follow-up. The mortality rate was 74% (n=11) and the mean survival rate was 79.7 months (in between 5-312 months). Multi-visceral organ transplantation was performed to one patient. Conclusion: Following prophylactic colectomy at early ages, desmoid tumor has been the most common reason of the mortality in Polyposis syndrome. At the time of diagnosis, most patients are inoperable because of the invasion to adjacent organs, especially small-bowel meso. Although multi-visceral organ transplantation is one of the most complicated surgical procedures, it seems to be a convenient treatment option in patients with desmoid tumor.

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