Abstract:

Epidermolysis Bullosa (EB); It is a systemic, inherited and chronic autoimmune disease. The disease can affect both genders, regardless of race and ethnic group; It progresses with blisters-filled with water in different parts of the body such as hands, feet, legs, esophagus, and oral mucosa. It is a disease that seen in 19 infants per one million live births. The clinical picture of children with EB is very severe; Morbidity and mortality rates are high due to increased bullae in the mucosa of vital organs. The disease can affect all organs of the body systemically. In chronic diseases, pediatric nurses have important responsibilities in order to ensure the adaptation of the child and family members to the disease, to maintain their care and to increase their quality of life. Take care at this stage, nursing theories and models are used in order to increase its effectiveness , systematize, create a guide and increase it professionalism. There are a lımıted number of studıes ın the literatüre, in which Roper Logan Tierney's Nursing Model Based on Life Activities Nursing Model is used in the care of children with chronic diseases. In this case report, the nursing care of a child diagnosed with EB, which is a rare case disease, care is provided with reference to Roper Logan Tierney's Nursing Model Based on Life Activities Nursing Model. In the analysis of the case, a care plan was created by considering 6 specific activities (Ensuring the Safety of the Patient and His Environment, maintaining communication, nutrition, evacuation, individual cleaning and dressing, death) according to 12 life activity models, in which the addiction status was evaluated.

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