Özet:

Congenital diaphragmatic hernia is a relatively rare birth defect with unknown etiology. Its association with other anomalies and distinct clinical patterns suggest that several causes may be involved. Congenital diaphragmatic hernia occurs in 1 in 2500 live births. In 85% of cases the defect is left-sided [ 1]. Most cases of congenital diaphragmatic herniaare sporadic and familial congenital diaphragmatic herniais rare, comprising only 2% of congenital diaphragmatic herniacases[2]. This congenital anomaly can almost always be recognized with prenatal ultrasound screening. There is a high degree of variability in both treatment and outcomes. Bilateral congenital diaphragmatic hernia is a rare birth defect, with grim prognosis. We describe a case of bilateral congenital diaphragmatic hernia discovered while repartitioning right sided congenital diaphragmatic hernia. The diaphragmatic defect was repaired and a prolene mesh was placed on the abdominal wound to avoid abdominal compartment syndrome. The patient nonetheless died post operatively due to severe pulmonary hypertension. Bilateral congenital diaphragmatic hernia, priorly identified through a limited number of case reports, is extremely rare. The care of congenital diaphragmatic hernia patients is very difficult for neonatologists and surgeons. Our report particularly the management and outcome of patients with bilateral congenital diaphragmatic hernia.

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