Özet:

Hemolytic uremic syndrome (HUS) is a thrombotic microangiopathy characterized by intravascular hemolysis, thrombocytopenia and acute renal failure. HUS is generally classified into two types. While typical HUS follows a gastrointestinal infection with shiga-toxin producing E. coli (STEC), aHUS is associated with autoantibodies or mutations that lead to irregular complement activation. However, according to some recent studies, it was observed that diarrhea and multisystem involvement were seen in both HUS types. STEC positivity was also detected in a little percent of aHUS cases. Histopathological findings compatible with myocarditis were found in postmortem examinations in some cases. Although our case was diagnosed with atypical HUS, typical HUS symptoms such as bloody diarrhea and Shiga toxin 2 positivity were reported and myocardial involvement was observed as a rare complication.

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