Abstract:

Lymphangiomas are benign proliferations of the lymphatic system and superficial vascular malformation of lymphatic channels which is linked by endothelium. There are three known types of lymphangiomas: circumscriptum, cavernous, and cystic. The most common form of cutaneous lymphangioma is lymphangioma circumscriptum (LC). It is either congenital or acquired due to lymphatic obstruction. The most common localizations are the proximal parts of limbs, oral cavity, axilla, shoulders, groin, buttocks which contain extensive lymphatic network. Vulvar involvement is very rare. It is characterized by localized group of thin walled and translucent vesicles at varying sizes which are filled with clear lymphatic fluid. Vulvar LS can be associated with congenital lymphoedema in other parts of the body. Histopathology revealed large, irregular cystic dilatation and proliferation of lymphatic channels which contained proteinaceous fluid in the dermis. Biopsy is the gold standard method for the diagnosis. Differantial diagnosis of the vulvar LS includes Herpes zoster, condiloma accuminata, molloscum contagiosum, Kaposi's sarcoma, Buschke-Lowenstein tumor. Here, we aimed to introduce a primary vulvar LS in an elderly women. However, we also mentioned histopathological findings and differential diagnosis of this rare condition.

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