Abstract:

Caroli disease is a congenital, rare disease characterized by the cystic dilatation of the intrahepatic gland routes. The clinical characteristics of Caroli disease include yellowness, upper right neck pain, fever, which develops due to hepatolithiasis or bacterial collangitis. Endoscopic or percutaneous colanjiography is a traditional diagnosis method, but today magnetic resonance colanjiopankreatography has appeared as the preferred diagnosis tool. Treatment of Caroli disease; antibiotic therapy and support therapy for cholangitis, ursodeoxycolic acid treatment for hepatolithiasis. Localized caroli disease, which holds the lobe of the liver, is successfully applied to the surgical resection. The treatment should be selected by orthodotic liver transplant. We presented here the fact of Caroli, who was 58 years old, has been complaining of stomach pain for 3 years, with collangite attacks and was eventually treated with surgical resection. Caroli's disease is a rare congenital disease of the liver characterized by cystic dilatation of the intrahepatic even duct. The clinical features of Caroli's disease include yellowness, right upper abdominal pain and fever due to the associated complications of hepatolithiasis or bacterial cholangitis. Endoscopic or percutaneous cholangiography is the traditional method of diagnosis, but nowadays magnetic resonance cholangiopancreatography is emerging as the diagnostic modality of choice. The treatment for Caroli's disease includes supportive care with antibiotics for cholangitis and ursodeoxycholic acid for hepatolithiasis. Surgical resection has been used successfully in patients with monolobar disease. For patients with diffuse involvement, the treatment of choice is orthotopic liver transplantation. In this article, we report a 58 years old male patient with Caroli's disease. The patient had abdominal pain and episodes of cholangitis for 3 years and finally, he was treated with surgical resection. Key words : Caroli's disease, cystic dilation, cholangitis