Abstract:

Coronary artery anomalies may present as anomalies of origination, course and termination (eg.A-V fistula), and as coronary artery aneurysms. Coronary artery anomalies are rare entities, and are usually detected during angiograms or necropsy. The rate of congenital coronary artery anomalies is reported to be between 0.3% and 1.3% in adult patients underwent invasive coronary angiograpies and 1% in routine autopsy studies. Of them 87% were anomalies of origin and course and 13% were coronary artery fistulas. Although most of the cases with coronary artery anomalies were asymptomatic, ectopic origin and course of coronary artery between aorta and pulmonary artery were reported to be associated with myocardial ischemia and sudden cardiac death.We present a case who had left main coronary artery arising from the right sinus of Valsalva, which is a rare congenital anomaly; and we reviewed the literature.

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