Özet:

Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital disease, seen with uterus didelfis, blind hemivagen and ipsilateral renal agenesis. Sigmoid volvulus is commonly found in older people. It is a rare disease in adolescents and young people. There is no information in the literature that there is a relationship between HWW syndrome and sigmoid colon volvulus. In a young patient with congenital anomaly, the detection of sigmoid colon volvulus suggests that there can be a relationship between the two pathologies. In our study; stomach pain, swelling, abdominal nausea, gas and gaita with no removal complaints and the patient who applying for emergency service was diagnosed with sigmoid volvulus with a direct western graph, in emergency conditions, a colonoscopic decompression was done and the optional anterior resection operation was adjusted.