Özet:

The corpus callosum is the most important relay connection between the two hemispheres. The malformation of the corpus callosum manifests as total agenesis or dysgenesis of various degrees and these afflictions have highly variable clinical expression. Current imaging investigative possibilities allow the early detection of any malformations even in the fetal period. The cases in which brain malformation, either solitary or within a syndrome, associates with sensory or neural hearing loss are very rare. The authors present the case of a child with severe bilateral hearing loss and dysgenesis of the corpus callosum. The retrocochlear feature of hearing loss and the late identification of the malformative pathology of the brain is what gives the case its particularities.

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