Abstract:

In 1953 and 1954, Silver and Russell independently described groups of small children whose pregnancies had complicated by intrauterine growth retardation with a both genetically and clinically heterogeneous disorder named Russel Silver Syndrome [RSS/SRS; OMIM 180860]. This case report describes the dental complications of the syndrome. A 4-yearold girl diagnosed with RSS at  the Medical Faculty Hospital of  Marmara University was directed to Marmara University Department of Pediatric Dentistry for dental examination. Severe dentin caries and pulpitis were detected in many teeth of the primary dentition as an indication of the child being in the high caries risk group (dft/dfs = 13/37). RSS-diagnosed children first experience nutritional difficulty and later face severe dental caries as a consequence. 

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