Özet:

Hemolithic urethral syndrome (HUS) is a clinical picture characterized by hemolithic anemia, thrombocytopenia and acute renal failure. It is one of the most common causes of acute kidney failure in infants and children. There are two types of HUS. Typical HUS is the most common form in children, which develops depending on shigatoxine, which occurs after 90% diarrhoea or upper respiratory infection. Atipic HUS is a primary disease that develops associated with a disorder in the regulation of the complementary alternative pathway and is also known as non-shigatoxin-HUS. 5-10% of developing children are atypical HIV and 20% of these phenomena are accompanied by extra-renal diseases. In the first attack, the last period of kidney failure development and mortality rates are high. Immediate correction of hypertension, proper electrolyte and fluid treatment, early dialysis and nutritial support reduces mortality. Today, intensive plasma therapy is the most effective method of treatment. We also intended to discuss the intensive support therapy in HUS, plasmaferesis and long-term renal replacement therapy.

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