Özet:

Anthinotrophic cytoplasmic antibodies (ANCA) associated small vasculitis is a group of diseases that are the most serious and common symptoms of kidney retention and threaten life. Microscopic poliangitis (MPA) is a rare vasculitis in children, characterized by pauci-immun rapidly progressing glomerulonefritis and pulmonary-renal syndrome. A 9-year-old boy was placed in the clinic with a complaint of ejaculation, arthritis and urinary coloring. Proteinuria and hematuria were present in urine analysis. In the patient’s laboratory examination, anemia, renal insufficiency and p-ANCA positivity were identified. There was a common infiltration in Toraks BT. In the kidney biopsy there was cementic glomerulonefritis, the immunfloresan examination was negative. The patient was considered MPA with the existing findings. High doses of methyl prednisolone, high doses of cyclophosphamide were given treatment, significant improvements in kidney functions and lungs findings were observed.