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Tanıtım: Fasiyal pleksiform nörofibroma (FPN) yüzün nadir görülen tümörlerinden biridir. Kranial sinirler veya üst servikal sinirleri içerir ve lezyon düşük oranda malign transformasyon gösterir. Özellikle çocukluk çağında izlenir. FPN aynı zamanda nörofibromatozis tip 1 (NF1) için tanı kriterlerinden biridir. NF1 yaygın ve multisistemik bir sendromdur. Bu olgu raporunda, çocuk hastada FPN ile birlikte izlenen NF1'in oral ve radyografik bulgularının sunulması amaçlandı. Olgu Bildirimi: Dokuz yaşındaki NF1 tanılı erkek hasta sol mandibuler posterior bölgede yemek yerken gelişen ağrı şikayetiyle kliniğimize başvurdu. Ekstraoral muayenede ‘cafe-au-lait’ lekeleri ve sol yanakta ağrısız şişlik görüldü. Şişliğin palpasyonunda solucan torbası hissi alındı. İntraoral muayenede sol bukkal mukozada şişlik, alveoler kemikte genişleme ve bütün süt molar dişlerde çürükler olduğu saptandı. Periapikal radyografta 75 numaralı dişte enfeksiyon ve buna bağlı olarak distal kök rezorpsiyonu belirlendi. Panoramik radyografta mandibuler ramusta incelme, mandibuler kanal ağzında genişleme, mandibuler çentikte derinleşme ve koronoid proçeste ve kondil boynunda uzama izlendi. Alınan anamnez ve yapılan klinik ve radyografik muayene sonucunda yanaktaki şişliğin dental apseye bağlı olmadığı bununla birlikte bunun bir FPN lezyonu olduğu belirlendi. Hastanın gereken diş tedavileri yapıldı ve rutin kontrol randevuları oluşturuldu. Sonuç: Çocuk diş hekimliğinde fasiyal asimetrilerin klinik olarak değerlendirilmesinde dental patolojiler dışında kalan oluşumlara FPN’nin de sebep olabileceği akılda tutulmalıdır.
Facial plexiform neurophibroma (FPN) is a rare tumor appearing on the face. It involves cranial or upper cervical nerves, and lesions show malign transformation at a low rate. It is especially seen in childhood. FPN is also a component of the diagnostic criteria for type 1 neurofibromatosis (NF1). NF1 is a common and multi-systemic syndrome. This case report aimed at presenting the oral and radiographic findings of FPN and NF1 diagnosed in a child patient. Case Report: A 9-year-old male patient diagnosed with NF1 applied to our clinic complaining from pain during eating in the left mandibular posterior region. Extraoral examination showed 'cafe-au-lait' blots and an asymptomatic swelling on the left cheek. Worm-bag-sensation was felt on palpation of the swelling. Intraoral examination showed swelling of the buccal mucosa, enlargement in the alveolar ridge and caries on all primary molar teeth. Periapical radiograph showed signs of infection and distal root resorption in tooth number 75. Panoramic radiograph revealed thinning of the mandibular ramus, dilatation of the mandibular foramen, deepening of the mandibular notch and prolongation of the coronoid process and condylar neck. The collected anamnesis together with the clinical and radiographic findings suggested that the swelling on the cheek was not due to a dental abscess; rather it was due to an FPN injury. The patient's treatment was done and routine check-up appointments were arranged. Conclusion: During clinical evaluation, it should be kept in mind that FPN may be one of the reasons for facial asymmetries of non-odontogenic pathologies in pediatric dentistry.
Introduction: Facial plexiform neurofibroma (FPN) is a rare tumor appearing on the face. It involves cranial or upper cervical nerves, and lesions show malign transformation at a low rate. It is especially seen in childhood. FPN is also a component of the diagnostic criteria for neurofibromatosis type 1 (NF1). NF1 is a common and multi-systemic syndrome. This case report aimed to present the oral and radiographic findings of FPN and NF1 diagnosed in a child patient. Case Report: A 9-year-old male patient diagnosed with NF1 applied to our clinic complaining from pain during eating in the left mandibular posterior region. Extraoral examination showed ‘cafe-au-lait’ blots and an asymptomatic swelling on the left cheek. Worm-bag-sensation was felt on palpation of the swelling. Intraoral examination showed swelling of the buccal mucosa, enlargement in the alveolar ridge and caries on all primary molar teeth. Periapical radiograph showed signs of infection and distal root resorption in tooth number 75. Panoramic radiograph revealed thinning of the mandibular ramus, dilatation of the mandibular foramen, deepening of the mandibular notch and prolongation of the coronoid process and condylar neck. The collected anamnesis together with the clinical and radiographical findings suggested that the swelling on the cheek was not due to a dental abscess; rather it was due to an FPN lesion. The patient's treatment was done and routine check-up appointments were arranged. Conclusion: During clinical evaluation, it should be kept in mind that FPN may be one of the reasons of facial asymmetries of non-odontogenic pathologies in pediatric dentistry.
Alan : Sağlık Bilimleri
Dergi Türü : Ulusal
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