Abstract:

Ataksi telenjektasis (AT) is an autosomal resessive transitional immune failure syndrome. Among the telenjiectases that can be seen in various places of the body, mesh wall telenjiectases are rarely seen and can cause life-threatening hematurial attacks. Our case was diagnosed with acute lymphoblastic leukemia alongside AT and was assessed by an endocrine hematurial clinic. In the diagnosed sistouretroscopy, common hemorrhagic telenjiectasis areas were observed in the bladder. The bleeding, fulguration and tranexamic acid caused by telegectasis were controlled by continuous infusion of intravenously. As a result, although there are different treatment options in hematurial patients with AT, the application of intravenous traneksamic acid with early systuretroscopy and subsequent fulguration of telenjiectases is effective in ensuring blood control.

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