Özet:

Herediter thyrocinemia type 1 (HT1) is a rare hereditary metabolic disease caused by a lack of hydrolase enzyme. In the administration of hereditary thyrocinemia type 1, it is recommended to use nitinone therapy along with a diet limited to thyrocin and phenylalan. Typ-1 diabetes mellitus (T1DM), also known as autoimmune diabetes, is a chronic endocrinological disease characterized by absolute insulin deficiency associated with pancreatic β-cell dysfunction and leading to hyperglycemia. Nutrition therapy and proper physical activity together with insulin play an important role in ensuring glycemic control in patients. A limited number of facts in literature have identified the HT1 and T1DM unity. In this presentation, the diet management and monitoring process of a developing phenomenon of T1DM is shared while the thyroxine metabolism disorders are monitored due to HT1. With intensive insulin treatment, phenylalanine and thyrozy-limited dietary treatment have been successfully managed in the combination of two diseases.

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