Özet:

The Mayer-Rokitansky-Küster-Hauser syndrome is a rare disorder affecting women with normal karyotype and ovarian function. It is characterized by partial or total aplasia of the uterus and two thirds of the vagina. The main symptom is a primary amenorrhea and absence of the uterus which are diagnosed during examination and imagery. This paper reports the case of a 20 year-old woman diagnosed with the MRKH syndrome and discusses its psychological, fertility and sexual intercourse impact on patients. A large number of studies have been conducted to improve the management of patients. This article presents these studies and treatment options like a neovagina or a human uterine allotransplantation. 

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